[1]赵家耀,孙希文.先天性脐膨出的发病机制及诊治研究[J].医学信息,2022,35(07):30-33.[doi:10.3969/j.issn.1006-1959.2022.07.008]
 ZHAO Jia-yao,SUN Xi-wen.The Pathogenesis, Diagnosis and Treatment of Congenital Omphalocele[J].Medical Information,2022,35(07):30-33.[doi:10.3969/j.issn.1006-1959.2022.07.008]
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先天性脐膨出的发病机制及诊治研究()
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医学信息[ISSN:1006-1959/CN:61-1278/R]

卷:
35卷
期数:
2022年07期
页码:
30-33
栏目:
综述
出版日期:
2022-04-01

文章信息/Info

Title:
The Pathogenesis, Diagnosis and Treatment of Congenital Omphalocele
文章编号:
1006-1959(2022)07-0030-04
作者:
赵家耀孙希文
(浙江大学医学院附属第二医院产科,浙江 杭州 310000)
Author(s):
ZHAO Jia-yaoSUN Xi-wen
(Department of Obstetrics,the Second Affiliated Hospital Zhejiang University School of Medicine,Hangzhou 310000,Zhejiang,China)
关键词:
脐膨出围产期管理染色体异常
Keywords:
OmphalocelePerinatal managementChromosome abnormality
分类号:
R722
DOI:
10.3969/j.issn.1006-1959.2022.07.008
文献标志码:
A
摘要:
脐膨出是先天性腹壁缺损的一种,其具体发病机制目前尚不明确,可能与腹侧体壁的发育相关,染色体异常及母体因素可能也在其中起到一定作用。小型脐膨出可以选择经阴道分娩,而巨大脐膨出一般选择剖宫产娩出胎儿。脐膨出的治疗以手术治疗为主,小型脐膨出一般能够进行Ⅰ期修复,大型脐膨出可采用Silo袋减张分期手术,未合并其他系统异常的患儿总体预后较好。本文就脐膨出的发病机制、诊断方法、治疗方法及预后情况作一综述。
Abstract:
Omphalocele is a kind of congenital abdominal wall defect, its specific pathogenesis is still unclear, which may be related to the development of ventral body wall, and chromosome abnormalities and maternal factors may also play a role in it. Small omphalocele can choose vaginal delivery, and giant omphalocele generally choose cesarean delivery. The treatment of omphalocele is mainly surgical treatment. Small omphalocele can generally be repaired in stage Ⅰ, while giant omphalocele can be treated by Silo bag stretch reduction and staging surgery. The overall prognosis of children without other systemic abnormalities is good. This article reviews the pathogenesis, diagnosis, treatment and prognosis of omphalocele.

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更新日期/Last Update: 1900-01-01