[1]张 婷.噬血细胞综合征治疗进展[J].医学信息,2019,32(22):46-48.[doi:10.3969/j.issn.1006-1959.2019.22.015]
　ZHANG Ting.Progress in the Treatment of Hemophagocytic Syndrome[J].Journal of Medical Information,2019,32(22):46-48.[doi:10.3969/j.issn.1006-1959.2019.22.015]
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噬血细胞综合征治疗进展()
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医学信息[ISSN:1006-1959/CN:61-1278/R]

卷:
32卷
期数:
2019年22期
页码:
46-48
栏目:
综述
出版日期:
2019-11-15

文章信息/Info

Title:
Progress in the Treatment of Hemophagocytic Syndrome
文章编号:
1006-1959（2019）22-0046-03
作者:
张 婷
（天津市儿童医院血液科，天津 300000）
Author(s):
ZHANG Ting
(Department of Hematology,Tianjin Children's Hospital,Tianjin 300000,China)
关键词:
噬血细胞综合征; 免疫; 炎症反应
Keywords:
Hemophagocytic syndrome; Immunity; Inflammatory response
分类号:
R725.5
DOI:
10.3969/j.issn.1006-1959.2019.22.015
文献标志码:
A
摘要:
噬血细胞综合征（HPS）又称为噬血细胞性淋巴组织细胞增生症，是一种病理性免疫激活引起过度炎症反应的临床综合征，临床分为继发性和原发性。由于病因多，发病机制复杂，临床表现多样化，诊断难度大，漏诊、误诊的可能性大。本文就HPS的病因、发病机制、诊断及治疗等方面的研究进展进行综述，以期为临床诊治HPS提供一定的理论依据。
Abstract:
Hemophagocytic syndrome (HPS), also known as hemophagocytic lymphohistiocytosis, is a clinical syndrome in which pathological immune activation causes excessive inflammatory response, clinically divided into secondary and primary. Due to many causes, the pathogenesis is complicated, the clinical manifestations are diversified, the diagnosis is difficult, and the possibility of missed diagnosis and misdiagnosis is high. This article reviews the research progress in the etiology, pathogenesis, diagnosis and treatment of HPS, in order to provide a theoretical basis for clinical diagnosis and treatment of HPS.

参考文献/References:

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更新日期/Last Update: 2019-11-15